Presentation of Ebstein's Anomaly in Adulthood: Case Report
DOI:
https://doi.org/10.55204/trc.v3i2.e229Keywords:
Ebstein Anomaly, Tricuspid Valve, Dyspnea, EchocardiographyAbstract
Introduction: Ebstein's anomaly represents a rare congenital malformation characterized by the attachment of the tricuspid valve in the right ventricular cavity, which produces atrialization of said ventricle.
Presentation of the case: A 35-year-old female patient who for approximately 1 year has presented dyspnea on great exertion accompanied by irritability and general malaise. The physical examination revealed a holosystolic murmur in a tricuspid focus with an intensity of 3/6 on the Levine scale. An echocardiogram was performed where the presence of low implantation of the tricuspid valve annulus and severe tricuspid regurgitation that produced pulmonary hypertension were observed.
Discussion: It is important to study the patient completely, which includes history, comorbidities, physical examination, and complementary tests that make it possible to adequately define the optimal treatment to be established, be it clinical, electrophysiological, hemodynamic, and/or surgical treatment. According to the literature, many authors consider that the optimal treatment should be early surgical treatment, before the clinical picture exacerbates.
Conclusions: Ebstein's anomaly is a low-incidence cardiac malformation. In our environment, this pathology is underdiagnosed in adult patients and is diagnosed in most cases as an incidental finding.
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